Q87.0
Congenital malformation syndromes predominantly affecting facial appearance
Q87.0 (also written Q870) is a billable ICD-10-CM diagnosis code for congenital malformation syndromes predominantly affecting facial appearance. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 21 codes in category Q87 (Other specified congenital malformation syndromes affecting multiple systems). The Alphabetic Index lists it under 39 entries. Its coding notes include a Use additional code instruction and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code(s) to identify all associated manifestations
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Other clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026Inclusion terms
Conditions classified to this code.
- Acrocephalopolysyndactyly
- Acrocephalosyndactyly [Apert]
- Cryptophthalmos syndrome
- Cyclopia
- Goldenhar syndrome
- Moebius syndrome
- Oro-facial-digital syndrome
- Robin syndrome
- Whistling face
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 39 entries
- Acrocephalopolysyndactyly
- Acrocephalosyndactyly
- Aglossia-adactylia syndrome
- Apert's syndrome
- Carpenter's syndrome
- Cryptophthalmos, syndrome
- Cyclopia, cyclops
- Cyclopism
- Dyscranio-pygo-phalangy
- Dysplasia, oculodentodigital
- Fraser's syndrome
- Freeman Sheldon syndrome
Show 27 more
- Goldenhar (-Gorlin) syndrome
- Gorlin-Chaudry-Moss syndrome
- Hallerman-Streiff syndrome
- Hanhart's syndrome
- Marchesani (-Weill) syndrome
- Meyer-Schwickerath and Weyers syndrome
- Moebius, Möbius, syndrome
- Moebius, Möbius, syndrome, congenital oculofacial paralysis (with other anomalies)
- Mohr's syndrome (Types I and II)
- Papillon-Léage and Psaume syndrome
- Paralysis, paralytic (complete) (incomplete), oculofacial, congenital (Moebius)
- Pierre Robin deformity or syndrome
- Robin (-Pierre) syndrome
- Syndrome, congenital, facial diplegia
- Syndrome, congenital, oculo-auriculovertebral
- Syndrome, congenital, oculofacial diplegia (Moebius)
- Syndrome, cryptophthalmos
- Syndrome, eyelid-malar-mandible
- Syndrome, first arch
- Syndrome, micrognathia-glossoptosis
- Syndrome, oral-facial-digital
- Syndrome, oro-facial-digital
- Syndrome, oto-palatal-digital
- Syndrome, whistling face
- Tower skull, with exophthalmos
- Ullrich-Feichtiger syndrome
- Whistling face