Q87.1

Congenital malformation syndromes predominantly associated with short stature

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/Q80–Q89 Other congenital malformations

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

Q87.1 is a non-billable ICD-10-CM code header for congenital malformation syndromes predominantly associated with short stature. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q87.11 Prader-Willi syndrome and Q87.19 Other congenital malformation syndromes predominantly associated with short stature. Its coding notes include a Use additional code instruction, 2 Excludes1 entries and 1 Excludes2 entry.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Use additional code

Add the listed code as a secondary code, if known.

Inherited from Q87 Other specified congenital malformation syndromes affecting multiple systems
  • code(s) to identify all associated manifestations

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • Ellis-van Creveld syndrome (Q77.6)
  • Smith-Lemli-Opitz syndrome (E78.72)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

More specific codes under Q87.1 2