Q87.8
Other specified congenital malformation syndromes, not elsewhere classified
Q87.8 is a non-billable ICD-10-CM code header for other specified congenital malformation syndromes, not elsewhere classified. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q87.81 Alport syndrome, Q87.82 Arterial tortuosity syndrome, Q87.83 Bardet-Biedl syndrome, Q87.84 Laurence-Moon syndrome and 5 more. Its coding notes include a Use additional code instruction, 1 Excludes1 entry and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code(s) to identify all associated manifestations
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- Zellweger syndrome (E71.510)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
More specific codes under Q87.8 9
- Q87.81Alport syndromeBillable
- Q87.82Arterial tortuosity syndromeBillable
- Q87.83Bardet-Biedl syndromeBillable
- Q87.84Laurence-Moon syndromeBillable
- Q87.85MED13L syndromeBillable
- Q87.86Kleefstra syndromeBillable
- Q87.87Hao-Fountain SyndromeBillable
- Q87.88CTNNB1 syndromeBillable
- Q87.89Other specified congenital malformation syndromes, not elsewhere classifiedBillable