Q87
Other specified congenital malformation syndromes affecting multiple systems
Q87 is a non-billable ICD-10-CM code category for other specified congenital malformation syndromes affecting multiple systems. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q87.0 Congenital malformation syndromes predominantly affecting facial appearance, Q87.1 Congenital malformation syndromes predominantly associated with short stature, Q87.2 Congenital malformation syndromes predominantly involving limbs, Q87.3 Congenital malformation syndromes involving early overgrowth and 4 more. Its coding notes include a Use additional code instruction and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code(s) to identify all associated manifestations
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
More specific codes under Q87 8
- Q87.0Congenital malformation syndromes predominantly affecting facial appearanceBillable
- Q87.1Congenital malformation syndromes predominantly associated with short statureHeader
- Q87.2Congenital malformation syndromes predominantly involving limbsBillable
- Q87.3Congenital malformation syndromes involving early overgrowthBillable
- Q87.4Marfan syndromeHeader
- Q87.5Other congenital malformation syndromes with other skeletal changesBillable
- Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedHeader
- Q87.ALoeys-Dietz syndromeBillable