Q87.4
Marfan syndrome
Q87.4 is a non-billable ICD-10-CM code header for marfan syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q87.40 Marfan syndrome, unspecified; Q87.41 Marfan syndrome with cardiovascular manifestations; Q87.42 Marfan syndrome with ocular manifestations and Q87.43 Marfan syndrome with skeletal manifestation. Its coding notes include a Use additional code instruction and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code(s) to identify all associated manifestations
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records