E84.1

Cystic fibrosis with intestinal manifestations

FY2027Chapter 4: Endocrine, nutritional and metabolic diseases/E70–E88 Metabolic disorders

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

E84.1 is a non-billable ICD-10-CM code header for cystic fibrosis with intestinal manifestations. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E84.11 Meconium ileus in cystic fibrosis and E84.19 Cystic fibrosis with other intestinal manifestations. Its coding notes include a Code also instruction, 6 Excludes1 entries and 1 Excludes2 entry.

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Inherited from E84 Cystic fibrosis
  • exocrine pancreatic insufficiency (K86.81)

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Also from chapter/block level (6 notes)
Inherited from E70–E88 Metabolic disorders
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (1 note)
Inherited from E70–E88 Metabolic disorders
  • Ehlers-Danlos syndromes (Q79.6-)

Includes

Further defines or gives examples of the content of the category.

Inherited from E84 Cystic fibrosis
  • mucoviscidosis

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

More specific codes under E84.1 2