E75
Disorders of sphingolipid metabolism and other lipid storage disorders
E75 is a non-billable ICD-10-CM code category for disorders of sphingolipid metabolism and other lipid storage disorders. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E75.0 GM2 gangliosidosis; E75.1 Other and unspecified gangliosidosis; E75.2 Other sphingolipidosis; E75.3 Sphingolipidosis, unspecified and 3 more. Its coding notes include 8 Excludes1 entries and 1 Excludes2 entry.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Also from chapter/block level (6 notes)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Notes
Also from chapter/block level (1 note)
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 2 entries
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), cerebral lipidoses
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), cerebral lipidoses, with behavioral disturbance