E78.7
Disorders of bile acid and cholesterol metabolism
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
E78.7 is a non-billable ICD-10-CM code header for disorders of bile acid and cholesterol metabolism. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E78.70 Disorder of bile acid and cholesterol metabolism, unspecified; E78.71 Barth syndrome; E78.72 Smith-Lemli-Opitz syndrome and E78.79 Other disorders of bile acid and cholesterol metabolism. Its coding notes include 8 Excludes1 entries and 1 Excludes2 entry.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
This code
- Niemann-Pick disease type C (E75.242)
Inherited from E78 Disorders of lipoprotein metabolism and other lipidemias
Also from chapter/block level (6 notes)
Inherited from E70–E88 Metabolic disorders
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Notes
Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.