N07.1

Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions

FY2027Chapter 14: Diseases of the genitourinary system/N00–N08 Glomerular diseases

BillableComplete code, valid to report

N07.1 (also written N071) is a billable ICD-10-CM diagnosis code for hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 12 codes in category N07 (Hereditary nephropathy, not elsewhere classified). The Alphabetic Index lists it under 1 entry. Its coding notes include a Code also instruction, 1 Excludes1 entry and 12 Excludes2 entries.

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Also from chapter/block level (1 note)
Inherited from N00–N08 Glomerular diseases
  • any associated kidney failure (N17-N19).

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Also from chapter/block level (1 note)
Inherited from N00–N08 Glomerular diseases
  • hypertensive chronic kidney disease (I12.-)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from N07 Hereditary nephropathy, not elsewhere classified
  • Alport's syndrome (Q87.81-)
  • hereditary amyloid nephropathy (E85.-)
  • nail patella syndrome (Q87.2)
  • non-neuropathic heredofamilial amyloidosis (E85.-)
Also from chapter/block level (8 notes)
Inherited from Chapter 14 Diseases of the genitourinary system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Other clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Inclusion terms

Conditions classified to this code.

This code
  • Hereditary nephropathy, not elsewhere classified with focal and segmental hyalinosis
  • Hereditary nephropathy, not elsewhere classified with focal and segmental sclerosis
  • Hereditary nephropathy, not elsewhere classified with focal glomerulonephritis

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 1 entry