N01
Rapidly progressive nephritic syndrome
N01 is a non-billable ICD-10-CM code category for rapidly progressive nephritic syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality, N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions, N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis, N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis and 7 more. Its coding notes include a Code also instruction, 2 Excludes1 entries and 8 Excludes2 entries.
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- nephritic syndrome NOS (N05.-)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (8 notes)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Includes
Further defines or gives examples of the content of the category.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
More specific codes under N01 11
- N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormalityBillable
- N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesionsBillable
- N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritisBillable
- N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
- N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
- N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
- N01.6Rapidly progressive nephritic syndrome with dense deposit diseaseBillable
- N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritisBillable
- N01.8Rapidly progressive nephritic syndrome with other morphologic changesBillable
- N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changesBillable
- N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritisBillable