N04
Nephrotic syndrome
N04 is a non-billable ICD-10-CM code category for nephrotic syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are N04.0 Nephrotic syndrome with minor glomerular abnormality, N04.1 Nephrotic syndrome with focal and segmental glomerular lesions, N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis, N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis and 8 more. Its coding notes include a Code also instruction, 1 Excludes1 entry and 8 Excludes2 entries.
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (8 notes)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Includes
Further defines or gives examples of the content of the category.
- congenital nephrotic syndrome
- lipoid nephrosis
More specific codes under N04 12
- N04.0Nephrotic syndrome with minor glomerular abnormalityBillable
- N04.1Nephrotic syndrome with focal and segmental glomerular lesionsBillable
- N04.2Nephrotic syndrome with diffuse membranous glomerulonephritisHeader
- N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
- N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
- N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
- N04.6Nephrotic syndrome with dense deposit diseaseBillable
- N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritisBillable
- N04.8Nephrotic syndrome with other morphologic changesBillable
- N04.9Nephrotic syndrome with unspecified morphologic changesBillable
- N04.ANephrotic syndrome with C3 glomerulonephritisBillable
- N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)Header