Alphabetic Index FY2027

G11.3

Cerebellar ataxia with defective DNA repair

FY2027Chapter 6: Diseases of the nervous system/G10–G14 Systemic atrophies primarily affecting the central nervous system

BillableComplete code, valid to report
Care settingsHome Health Primary · Neuro RehabilitationHospital CC

G11.3 (also written G113) is a billable ICD-10-CM diagnosis code for cerebellar ataxia with defective DNA repair. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 11 codes in category G11 (Hereditary ataxia). The Alphabetic Index lists it under 9 entries. Its coding notes include 14 Excludes2 entries.

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

This code
  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)
Inherited from G11 Hereditary ataxia
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)
Also from chapter/block level (8 notes)
Inherited from Chapter 6 Diseases of the nervous system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the Neuro Rehabilitation clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Hospital CC

Counts as a complication or comorbidity (CC) when reported as a secondary diagnosis on an inpatient claim. It does not count when the principal diagnosis is one of the 175 codes in its exclusion list. Some MS-DRGs also ignore a CC or MCC that defines the DRG.

Source: CMS MS-DRG Definitions Manual v44, effective October 1, 2026, Appendix C

Inclusion terms

Conditions classified to this code.

This code
  • Ataxia telangiectasia [Louis-Bar]

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 9 entries