G11.1

Early-onset cerebellar ataxia

FY2027Chapter 6: Diseases of the nervous system/G10–G14 Systemic atrophies primarily affecting the central nervous system

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

G11.1 is a non-billable ICD-10-CM code header for early-onset cerebellar ataxia. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are G11.10 Early-onset cerebellar ataxia, unspecified; G11.11 Friedreich ataxia and G11.19 Other early-onset cerebellar ataxia. Its coding notes include 11 Excludes2 entries.

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from G11 Hereditary ataxia
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)
Also from chapter/block level (8 notes)
Inherited from Chapter 6 Diseases of the nervous system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

More specific codes under G11.1 3