E83.01
Wilson's disease
E83.01 (also written E8301) is a billable ICD-10-CM diagnosis code for wilson's disease. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 31 codes in category E83 (Disorders of mineral metabolism). The Alphabetic Index lists it under 26 entries. Its coding notes include a Code also instruction, 9 Excludes1 entries and 1 Excludes2 entry.
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
- associated Kayser Fleischer ring (H18.04-)
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- dietary mineral deficiency (E58-E61)
- parathyroid disorders (E20-E21)
- vitamin D deficiency (E55.-)
Also from chapter/block level (6 notes)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Other clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026Notes
Also from chapter/block level (1 note)
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 26 entries
- Cirrhosis, cirrhotic (hepatic) (liver), due to, hepatolenticular degeneration
- Cirrhosis, cirrhotic (hepatic) (liver), due to, Wilson's disease
- Deficiency, deficient, ceruloplasmin (Wilson)
- Degeneration, degenerative, hepatolenticular (Wilson's)
- Degeneration, degenerative, lenticular (familial) (progressive) (Wilson's) (with cirrhosis of liver)
- Degeneration, degenerative, Wilson's hepatolenticular
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), hepatolenticular degeneration
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety), in (due to), hepatolenticular degeneration, with behavioral disturbance
- Disease, diseased, hepatolenticular
- Disease, diseased, Kinnier Wilson's (hepatolenticular degeneration)
- Disease, diseased, Wilson's (hepatolenticular degeneration)
- Disorder (of), metabolism NOS, copper, Wilson's disease
Show 14 more
- Disorder (of), tubulo-interstitial (in), Wilson's disease
- Hepatolenticular degeneration
- Kinnier Wilson's disease (hepatolenticular degeneration)
- Lenticular degeneration, progressive
- Pseudosclerosis (brain), of Westphal (Strümpell)
- Pyelonephritis, in (due to), Wilson's disease
- Strümpell-Westphal pseudosclerosis
- Syndrome, amyostatic (Wilson's disease)
- Syndrome, lenticular, progressive
- Syndrome, Westphal-Strümpell
- Syndrome, Wilson's (hepatolenticular degeneration)
- Westphal-Strümpell syndrome
- Wilson's, disease or syndrome
- Wilson's, hepatolenticular degeneration