D70.0
Congenital agranulocytosis
D70.0 (also written D700) is a billable ICD-10-CM diagnosis code for congenital agranulocytosis. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 7 codes in category D70 (Neutropenia). The Alphabetic Index lists it under 10 entries. Its coding notes include a Use additional code instruction, a Code also instruction, 2 Excludes1 entries and 9 Excludes2 entries.
Use additional code
Add the listed code as a secondary code, if known.
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (9 notes)
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Infectious Disease, Neoplasms, and Blood-Forming Diseases clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026Includes
Further defines or gives examples of the content of the category.
- agranulocytosis
- decreased absolute neurophile count (ANC)
Inclusion terms
Conditions classified to this code.
- Congenital neutropenia
- Infantile genetic agranulocytosis
- Kostmann's disease
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 10 entries
- Agranulocytosis (chronic) (cyclical) (genetic) (infantile) (periodic) (pernicious), congenital
- Aleukia, congenital
- Disease, diseased, Kostmann's (infantile genetic agranulocytosis)
- Leukopenia, congenital
- Leukopenia, cyclic
- Leukopenia, familial
- Leukopenia, infantile genetic
- Leukopenia, periodic
- Neutropenia, neutropenic (chronic) (genetic) (idiopathic) (immune) (infantile) (malignant) (pernicious) (splenic), congenital (primary)
- Syndrome, Kostmann's