Q85.01
Neurofibromatosis, type 1
Q85.01 (also written Q8501) is a billable ICD-10-CM diagnosis code for neurofibromatosis, type 1. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 11 codes in category Q85 (Phakomatoses, not elsewhere classified). The Alphabetic Index lists it under 3 entries. Its coding notes include 2 Excludes1 entries and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the Neuro Rehabilitation clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026IPF Comorbidity
On the CMS IPF comorbidity list.
| Comorbidity category | Factor |
|---|---|
| Oncology Treatment | 1.44 |
Inclusion terms
Conditions classified to this code.
- Von Recklinghausen disease
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 3 entries