Q07.0

Arnold-Chiari syndrome

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/Q00–Q07 Congenital malformations of the nervous system

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

Q07.0 is a non-billable ICD-10-CM code header for arnold-Chiari syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q07.00 Arnold-Chiari syndrome without spina bifida or hydrocephalus, Q07.01 Arnold-Chiari syndrome with spina bifida, Q07.02 Arnold-Chiari syndrome with hydrocephalus and Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus. Its coding notes include 2 Excludes1 entries and 4 Excludes2 entries.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • Arnold-Chiari syndrome, type III (Q01.-)
  • Arnold-Chiari syndrome, type IV (Q04.8)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from Q07 Other congenital malformations of nervous system
  • congenital central alveolar hypoventilation syndrome (G47.35)
  • familial dysautonomia [Riley-Day] (G90.1)
  • neurofibromatosis (nonmalignant) (Q85.0-)
Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Inclusion terms

Conditions classified to this code.

This code
  • Arnold-Chiari syndrome, type II

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

More specific codes under Q07.0 4