Q01
Encephalocele
Q01 is a non-billable ICD-10-CM code category for encephalocele. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q01.0 Frontal encephalocele, Q01.1 Nasofrontal encephalocele, Q01.2 Occipital encephalocele, Q01.8 Encephalocele of other sites and 1 more. Its coding notes include 1 Excludes1 entry and 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- Meckel-Gruber syndrome (Q61.9)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
- inborn errors of metabolism (E70-E88)
Includes
Further defines or gives examples of the content of the category.
- Arnold-Chiari syndrome, type III
- encephalocystocele
- encephalomyelocele
- hydroencephalocele
- hydromeningocele, cranial
- meningocele, cerebral
- meningoencephalocele
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records