Q03

Congenital hydrocephalus

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/Q00–Q07 Congenital malformations of the nervous system

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

Q03 is a non-billable ICD-10-CM code category for congenital hydrocephalus. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q03.0 Malformations of aqueduct of Sylvius; Q03.1 Atresia of foramina of Magendie and Luschka; Q03.8 Other congenital hydrocephalus and Q03.9 Congenital hydrocephalus, unspecified. Its coding notes include 4 Excludes1 entries and 1 Excludes2 entry.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • Arnold-Chiari syndrome, type II (Q07.0-)
  • acquired hydrocephalus (G91.-)
  • hydrocephalus due to congenital toxoplasmosis (P37.1)
  • hydrocephalus with spina bifida (Q05.0-Q05.4)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Includes

Further defines or gives examples of the content of the category.

This code
  • hydrocephalus in newborn

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

More specific codes under Q03 4