Q00
Anencephaly and similar malformations
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
Q00 is a non-billable ICD-10-CM code category for anencephaly and similar malformations. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q00.0 Anencephaly, Q00.1 Craniorachischisis and Q00.2 Iniencephaly. Its coding notes include 1 Excludes2 entry.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- inborn errors of metabolism (E70-E88)
Notes
Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Codes from this chapter are not for use on maternal records