I01.9
Acute rheumatic heart disease, unspecified
I01.9 (also written I019) is a billable ICD-10-CM diagnosis code for acute rheumatic heart disease, unspecified. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 5 codes in category I01 (Rheumatic fever with heart involvement). The Alphabetic Index lists it under 5 entries. Its coding notes include 1 Excludes1 entry and 10 Excludes2 entries.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (10 notes)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Cardiac and Circulatory clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026Hospital CC
Counts as a complication or comorbidity (CC) when reported as a secondary diagnosis on an inpatient claim. It does not count when the principal diagnosis is one of the 34 codes in its exclusion list. Some MS-DRGs also ignore a CC or MCC that defines the DRG.
Source: CMS MS-DRG Definitions Manual v44, effective October 1, 2026, Appendix CInclusion terms
Conditions classified to this code.
- Any condition in I00 with unspecified type of heart involvement
- Rheumatic carditis, acute
- Rheumatic heart disease, active or acute
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 5 entries
- Bouillaud's disease or syndrome (rheumatic heart disease)
- Disease, diseased, Bouillaud's (rheumatic heart disease)
- Disease, diseased, heart (organic), rheumatic (chronic) (inactive) (old) (quiescent) (with chorea), active or acute
- Disease, diseased, heart (organic), with, rheumatic fever (conditions in I00), active
- Syndrome, Bouillaud's