I01

Rheumatic fever with heart involvement

FY2027Chapter 9: Diseases of the circulatory system/I00–I02 Acute rheumatic fever

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

I01 is a non-billable ICD-10-CM code category for rheumatic fever with heart involvement. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are I01.0 Acute rheumatic pericarditis, I01.1 Acute rheumatic endocarditis, I01.2 Acute rheumatic myocarditis, I01.8 Other acute rheumatic heart disease and 1 more. Its coding notes include 1 Excludes1 entry and 10 Excludes2 entries.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (10 notes)
Inherited from Chapter 9 Diseases of the circulatory system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 1 entry

More specific codes under I01 5