E71.54
Other peroxisomal disorders
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
E71.54 is a non-billable ICD-10-CM code header for other peroxisomal disorders. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E71.540 Rhizomelic chondrodysplasia punctata, E71.541 Zellweger-like syndrome, E71.542 Other group 3 peroxisomal disorders and E71.548 Other peroxisomal disorders. Its coding notes include 7 Excludes1 entries and 1 Excludes2 entry.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Also from chapter/block level (6 notes)
Inherited from E70–E88 Metabolic disorders
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Notes
Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.