E71.51
Disorders of peroxisome biogenesis
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
E71.51 is a non-billable ICD-10-CM code header for disorders of peroxisome biogenesis. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E71.510 Zellweger syndrome, E71.511 Neonatal adrenoleukodystrophy and E71.518 Other disorders of peroxisome biogenesis. Its coding notes include 8 Excludes1 entries and 1 Excludes2 entry.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
This code
- Refsum's disease (G60.1)
Also from chapter/block level (6 notes)
Inherited from E70–E88 Metabolic disorders
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Inclusion terms
Conditions classified to this code.
This code
- Group 1 peroxisomal disorders
Notes
Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.