E31.22

Multiple endocrine neoplasia [MEN] type IIA

FY2027Chapter 4: Endocrine, nutritional and metabolic diseases/E20–E35 Disorders of other endocrine glands

BillableComplete code, valid to report

E31.22 (also written E3122) is a billable ICD-10-CM diagnosis code for multiple endocrine neoplasia [MEN] type IIA. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 8 codes in category E31 (Polyglandular dysfunction). The Alphabetic Index lists it under 3 entries. Its coding notes include a Code also instruction and 6 Excludes1 entries.

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Inherited from E31.2 Multiple endocrine neoplasia [MEN] syndromes
  • any associated malignancies and other conditions associated with the syndromes

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Inherited from E31 Polyglandular dysfunction
  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • dystrophia myotonica [Steinert] (G71.11)
  • pseudohypoparathyroidism (E20.1)
Also from chapter/block level (3 notes)
Inherited from E20–E35 Disorders of other endocrine glands
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Endocrine clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Inclusion terms

Conditions classified to this code.

This code
  • Sipple's syndrome

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 3 entries