E03.1
Congenital hypothyroidism without goiter
E03.1 (also written E031) is a billable ICD-10-CM diagnosis code for congenital hypothyroidism without goiter. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 8 codes in category E03 (Other hypothyroidism). The Alphabetic Index lists it under 11 entries. Its coding notes include 3 Excludes1 entries.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Home Health Primary
Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Endocrine clinical group.
Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026Inclusion terms
Conditions classified to this code.
- Aplasia of thyroid (with myxedema)
- Congenital atrophy of thyroid
- Congenital hypothyroidism NOS
Notes
Also from chapter/block level (1 note)
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 11 entries
- Absence (of) (organ or part) (complete or partial), thyroid (gland) (acquired), congenital
- Agenesis, thyroid (gland)
- Aplasia, thyroid (congenital) (with myxedema)
- Athyrea (acquired), congenital
- Atrophy, atrophic (of), thyroid (gland) (acquired), congenital (with myxedema)
- Atrophy, atrophic (of), thyroid (gland) (acquired), with cretinism
- Hypoplasia, hypoplastic, thyroid (gland)
- Hypothyroidism (acquired), congenital (without goiter)
- Insufficiency, insufficient, thyroid (gland) (acquired), congenital
- Jaundice (yellow), newborn, due to or associated with, hypothyroidism, congenital
- Subthyroidism (acquired), congenital