E00

Congenital iodine-deficiency syndrome

FY2027Chapter 4: Endocrine, nutritional and metabolic diseases/E00–E07 Disorders of thyroid gland

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

E00 is a non-billable ICD-10-CM code category for congenital iodine-deficiency syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E00.0 Congenital iodine-deficiency syndrome, neurological type; E00.1 Congenital iodine-deficiency syndrome, myxedematous type; E00.2 Congenital iodine-deficiency syndrome, mixed type and E00.9 Congenital iodine-deficiency syndrome, unspecified. Its coding notes include a Use additional code instruction and 2 Excludes1 entries.

Use additional code

Add the listed code as a secondary code, if known.

This code
  • code (F70-F79) to identify associated intellectual disabilities.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • subclinical iodine-deficiency hypothyroidism (E02)
Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

More specific codes under E00 4