E00.9

Congenital iodine-deficiency syndrome, unspecified

FY2027Chapter 4: Endocrine, nutritional and metabolic diseases/E00–E07 Disorders of thyroid gland

BillableComplete code, valid to report

E00.9 (also written E009) is a billable ICD-10-CM diagnosis code for congenital iodine-deficiency syndrome, unspecified. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 4 codes in category E00 (Congenital iodine-deficiency syndrome). The Alphabetic Index lists it under 3 entries. Its coding notes include a Use additional code instruction and 2 Excludes1 entries.

Use additional code

Add the listed code as a secondary code, if known.

Inherited from E00 Congenital iodine-deficiency syndrome
  • code (F70-F79) to identify associated intellectual disabilities.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Inherited from E00 Congenital iodine-deficiency syndrome
  • subclinical iodine-deficiency hypothyroidism (E02)
Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Endocrine clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Inclusion terms

Conditions classified to this code.

This code
  • Congenital iodine-deficiency hypothyroidism NOS
  • Endemic cretinism NOS

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 4 Endocrine, nutritional and metabolic diseases
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 3 entries