D68.02

Von Willebrand disease, type 2

FY2027Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism/D65–D69 Coagulation defects, purpura and other hemorrhagic conditions

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

D68.02 is a non-billable ICD-10-CM code header for von Willebrand disease, type 2. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are D68.020 Von Willebrand disease, type 2A; D68.021 Von Willebrand disease, type 2B; D68.022 Von Willebrand disease, type 2M; D68.023 Von Willebrand disease, type 2N and 1 more. Its coding notes include 4 Excludes1 entries and 11 Excludes2 entries.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Inherited from D68.0 Von Willebrand disease
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
Inherited from D68 Other coagulation defects
  • abnormal coagulation profile NOS (R79.1)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from D68 Other coagulation defects
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Also from chapter/block level (9 notes)
Inherited from Chapter 3 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Inclusion terms

Conditions classified to this code.

This code
  • Qualitative defects of von Willebrand factor

More specific codes under D68.02 5