D68.0

Von Willebrand disease

FY2027Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism/D65–D69 Coagulation defects, purpura and other hemorrhagic conditions

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

D68.0 is a non-billable ICD-10-CM code header for von Willebrand disease. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are D68.00 Von Willebrand disease, unspecified; D68.01 Von Willebrand disease, type 1; D68.02 Von Willebrand disease, type 2; D68.03 Von Willebrand disease, type 3 and 2 more. Its coding notes include 4 Excludes1 entries and 11 Excludes2 entries.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
Inherited from D68 Other coagulation defects
  • abnormal coagulation profile NOS (R79.1)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from D68 Other coagulation defects
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Also from chapter/block level (9 notes)
Inherited from Chapter 3 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

More specific codes under D68.0 6