QA1.71

Lynch syndrome

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/QA0–QA1 Genetic disorders, not elsewhere classified

BillableComplete code, valid to report

QA1.71 (also written QA171) is a billable ICD-10-CM diagnosis code for lynch syndrome. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 5 codes in category QA1 (Genetic disorders associated with neoplasms, not elsewhere classified). The Alphabetic Index lists it under 2 entries. Its coding notes include a Code also instruction and 2 Excludes2 entries.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Inherited from QA1 Genetic disorders associated with neoplasms, not elsewhere classified
  • , if applicable, any associated conditions, such as:
    • genetic susceptibility to malignant neoplasm by site (Z15.0-)
    • malignant neoplasms (C00.0-C96.9)
    • personal history of malignant neoplasm (Z85.-)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from QA1 Genetic disorders associated with neoplasms, not elsewhere classified
  • multiple endocrine neoplasia [MEN] syndromes (E31.2-)
Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Inclusion terms

Conditions classified to this code.

This code
  • Hereditary nonpolyposis colorectal cancer susceptibility
  • Lynch syndrome due to EPCAM
  • Lynch syndrome due to MLH1
  • Lynch syndrome due to MSH2
  • Lynch syndrome due to MSH6
  • Lynch syndrome due to PMS2

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 2 entries