Q91.4

Trisomy 13, nonmosaicism (meiotic nondisjunction)

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/Q90–Q99 Chromosomal abnormalities, not elsewhere classified

BillableComplete code, valid to report

Q91.4 (also written Q914) is a billable ICD-10-CM diagnosis code for trisomy 13, nonmosaicism (meiotic nondisjunction). It is part of the FY2027 code set, effective October 1, 2026. It is one of the 8 codes in category Q91 (Trisomy 18 and Trisomy 13). The Alphabetic Index lists it under 2 entries. Its coding notes include 2 Excludes2 entries.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (2 notes)
Inherited from Q90–Q99 Chromosomal abnormalities, not elsewhere classified
  • mitochondrial metabolic disorders (E88.4-)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Other clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Hospital CC

Counts as a complication or comorbidity (CC) when reported as a secondary diagnosis on an inpatient claim. It does not count when the principal diagnosis is one of the 68 codes in its exclusion list. Some MS-DRGs also ignore a CC or MCC that defines the DRG.

Source: CMS MS-DRG Definitions Manual v44, effective October 1, 2026, Appendix C

IPF Primary

IPF MS-DRG adjustment. A principal diagnosis of this code groups to this MS-DRG:

MS-DRGDescriptionFactor
884Organic disturbances & intellectual disabilities1.08
A principal diagnosis that groups to none of the 19 designated MS-DRGs gets no MS-DRG adjustment. Otherwise the claim still receives the federal per diem base rate and the other adjustments.

Source: CMS IPF PPS FY 2027 final rule (CMS-1847-F), Addendum A; code lists from the CMS MS-DRG Definitions Manual v44; effective for discharges on or after October 1, 2026

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 2 entries