Q16.5
Congenital malformation of inner ear
Q16.5 (also written Q165) is a billable ICD-10-CM diagnosis code for congenital malformation of inner ear. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 7 codes in category Q16 (Congenital malformations of ear causing impairment of hearing). The Alphabetic Index lists it under 24 entries. Its coding notes include 1 Excludes1 entry and 8 Excludes2 entries.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (8 notes)
- cleft lip and cleft palate (Q35-Q37)
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
- congenital malformation of larynx (Q31.-)
- congenital malformation of lip NEC (Q38.0)
- congenital malformation of nose (Q30.-)
- congenital malformation of parathyroid gland (Q89.2)
- congenital malformation of thyroid gland (Q89.2)
- inborn errors of metabolism (E70-E88)
Inclusion terms
Conditions classified to this code.
- Congenital anomaly of membranous labyrinth
- Congenital anomaly of organ of Corti
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 24 entries
- Absence (of) (organ or part) (complete or partial), ear, congenital, inner
- Absence (of) (organ or part) (complete or partial), inner ear, congenital
- Absence (of) (organ or part) (complete or partial), labyrinth, membranous
- Absence (of) (organ or part) (complete or partial), organ, of Corti, congenital
- Agenesis, labyrinth, membranous
- Agenesis, organ, of Corti
- Anomaly, anomalous (congenital) (unspecified type), ear (external), inner
- Anomaly, anomalous (congenital) (unspecified type), labyrinth, membranous
- Anomaly, anomalous (congenital) (unspecified type), organ, of Corti
- Aplasia, labyrinth, membranous
- Collapse, labyrinth, membranous (congenital)
- Deformity, ear (acquired), congenital (external), internal
Show 12 more
- Deformity, organ of Corti (congenital)
- Degeneration, degenerative, membranous labyrinth, congenital (causing impairment of hearing)
- Degeneration, degenerative, saccule, congenital (causing impairment of hearing)
- Dilatation, saccule, congenital
- Distortion (s) (congenital), ear (auricle) (external), inner
- Distortion (s) (congenital), organ, of Corti
- Enlargement, enlarged, vestibular aqueduct
- Malformation (congenital), cochlea
- Malformation (congenital), ear, inner
- Malformation (congenital), internal ear
- Malformation (congenital), Mondini's (congenital) (malformation, cochlea)
- Mondini's malformation (cochlea)