Q13.81
Rieger anomaly
Q13.81 (also written Q1381) is a billable ICD-10-CM diagnosis code for rieger anomaly. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 9 codes in category Q13 (Congenital malformations of anterior segment of eye). The Alphabetic Index lists it under 4 entries. Its coding notes include a Use additional code instruction, a Code also instruction and 8 Excludes2 entries.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code for associated glaucoma (H42)
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
- any other associated congenital malformations such as cardiac defects
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (8 notes)
- cleft lip and cleft palate (Q35-Q37)
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
- congenital malformation of larynx (Q31.-)
- congenital malformation of lip NEC (Q38.0)
- congenital malformation of nose (Q30.-)
- congenital malformation of parathyroid gland (Q89.2)
- congenital malformation of thyroid gland (Q89.2)
- inborn errors of metabolism (E70-E88)
Inclusion terms
Conditions classified to this code.
- Axenfeld-Rieger syndrome
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 4 entries