K00.5

Hereditary disturbances in tooth structure, not elsewhere classified

FY2027Chapter 11: Diseases of the digestive system/K00–K14 Diseases of oral cavity and salivary glands

BillableComplete code, valid to report

K00.5 (also written K005) is a billable ICD-10-CM diagnosis code for hereditary disturbances in tooth structure, not elsewhere classified. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 10 codes in category K00 (Disorders of tooth development and eruption). The Alphabetic Index lists it under 10 entries. Its coding notes include 9 Excludes2 entries.

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from K00 Disorders of tooth development and eruption
  • embedded and impacted teeth (K01.-)
Also from chapter/block level (8 notes)
Inherited from Chapter 11 Diseases of the digestive system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Inclusion terms

Conditions classified to this code.

This code
  • Amelogenesis imperfecta
  • Dentinogenesis imperfecta
  • Odontogenesis imperfecta
  • Dentinal dysplasia
  • Shell teeth

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 10 entries