J84.843

Alveolar capillary dysplasia with vein misalignment

FY2027Chapter 10: Diseases of the respiratory system/J80–J84 Other respiratory diseases principally affecting the interstitium

BillableComplete code, valid to report

J84.843 (also written J84843) is a billable ICD-10-CM diagnosis code for alveolar capillary dysplasia with vein misalignment. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 24 codes in category J84 (Other interstitial pulmonary diseases). The Alphabetic Index lists it under 1 entry. Its coding notes include a Use additional code instruction, a Code also instruction, 4 Excludes1 entries and 10 Excludes2 entries.

Use additional code

Add the listed code as a secondary code, if known.

Also from chapter/block level (7 notes)
Inherited from Chapter 10 Diseases of the respiratory system
  • code, where applicable, to identify:
    • exposure to environmental tobacco smoke (Z77.22)
    • exposure to tobacco smoke in the perinatal period (P96.81)
    • history of tobacco dependence (Z87.891)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Inherited from J84 Other interstitial pulmonary diseases
  • , if applicable, associated condition

Excludes1

Not coded here. The listed conditions generally should not be reported together.

Inherited from J84.8 Other specified interstitial pulmonary diseases
  • exogenous lipoid pneumonia (J69.1)
  • unspecified lipoid pneumonia (J69.1)
Inherited from J84 Other interstitial pulmonary diseases
  • drug-induced interstitial lung disorders (J70.2-J70.4)
  • interstitial emphysema (J98.2)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from J84 Other interstitial pulmonary diseases
  • lung diseases due to external agents (J60-J70)
Also from chapter/block level (9 notes)
Inherited from Chapter 10 Diseases of the respiratory system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • smoke inhalation (T59.81-)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Respiratory clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

Hospital MCC

Counts as a major complication or comorbidity (MCC) when reported as a secondary diagnosis on an inpatient claim. It does not count when the principal diagnosis is one of the 78 codes in its exclusion list. Some MS-DRGs also ignore a CC or MCC that defines the DRG.

Source: CMS MS-DRG Definitions Manual v44, effective October 1, 2026, Appendix C

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 10 Diseases of the respiratory system
  • When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 1 entry