J84.178
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
J84.178 (also written J84178) is a billable ICD-10-CM diagnosis code for other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 24 codes in category J84 (Other interstitial pulmonary diseases). The Alphabetic Index lists it under 12 entries. Its coding notes include a Code first instruction, a Use additional code instruction, a Code also instruction, 3 Excludes1 entries and 10 Excludes2 entries.
Code first
If the underlying condition listed here is present and known, sequence it first.
Use additional code
Add the listed code as a secondary code, if known.
Also from chapter/block level (7 notes)
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
- , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
- , if applicable, associated condition
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
- lung diseases due to external agents (J60-J70)
Also from chapter/block level (9 notes)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- smoke inhalation (T59.81-)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Hospice: not accepted as primary
Not accepted as the principal diagnosis on a hospice claim (bill types 081x and 082x). The Integrated OCE returns an edit for this code.
Reason: Manifestation code. Report the underlying condition first (see the Code first note).
Inclusion terms
Conditions classified to this code.
- Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
- Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
- Organizing pneumonia due to collagen vascular disease
- Organizing pneumonia in diseases classified elsewhere
Notes
Also from chapter/block level (1 note)
- When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 12 entries
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, due to, collagen vascular disease
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, due to, known underlying cause
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, in disease classified elsewhere
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, lymphocytic (due to collagen vascular disease) (in diseases classified elsewhere)
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, non-specific, due to, collagen vascular disease
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, non-specific, due to, known underlying cause
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, non-specific, in diseases classified elsewhere
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, usual, due to collagen vascular disease
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), interstitial, usual, in diseases classified elsewhere
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), organizing, due to, collagen vascular disease
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), organizing, due to, known underlying cause
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved), organizing, in diseases classified elsewhere