H57.01

Argyll Robertson pupil, atypical

FY2027Chapter 7: Diseases of the eye and adnexa/H55–H57 Other disorders of eye and adnexa

BillableComplete code, valid to report

H57.01 (also written H5701) is a billable ICD-10-CM diagnosis code for argyll Robertson pupil, atypical. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 24 codes in category H57 (Other disorders of eye and adnexa). The Alphabetic Index lists it under 1 entry. Its coding notes include 1 Excludes1 entry and 11 Excludes2 entries.

Excludes1

Not coded here. The listed conditions generally should not be reported together.

This code
  • syphilitic Argyll Robertson pupil (A52.19)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (11 notes)
Inherited from Chapter 7 Diseases of the eye and adnexa
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury (trauma) of eye and orbit (S05.-)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Care settings

How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.

Home Health Primary

Accepted as the primary (principal) diagnosis on a home health claim. The Home Health Grouper assigns it to the MMTA - Other clinical group.

Source: CMS Home Health Grouper Software v07.2.26, effective October 1, 2026

IPF Primary

IPF MS-DRG adjustment. A principal diagnosis of this code groups to one of these MS-DRGs. Which one depends on other facts of the stay, so the factor is a range:

MS-DRGDescriptionFactor
056Degenerative nervous system disorders w MCC1.12
057Degenerative nervous system disorders w/o MCC1.11
A principal diagnosis that groups to none of the 19 designated MS-DRGs gets no MS-DRG adjustment. Otherwise the claim still receives the federal per diem base rate and the other adjustments.

Source: CMS IPF PPS FY 2027 final rule (CMS-1847-F), Addendum A; code lists from the CMS MS-DRG Definitions Manual v44; effective for discharges on or after October 1, 2026

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 7 Diseases of the eye and adnexa
  • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Alphabetic Index terms

Terms the official Alphabetic Index lists for this code. 1 entry