G99.0
Autonomic neuropathy in diseases classified elsewhere
G99.0 (also written G990) is a billable ICD-10-CM diagnosis code for autonomic neuropathy in diseases classified elsewhere. It is part of the FY2027 code set, effective October 1, 2026. It is one of the 3 codes in category G99 (Other disorders of nervous system in diseases classified elsewhere). The Alphabetic Index lists it under 6 entries. Its coding notes include a Code first instruction, 1 Excludes1 entry and 8 Excludes2 entries.
Code first
If the underlying condition listed here is present and known, sequence it first.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- diabetic autonomic neuropathy (E08-E13 with .43)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (8 notes)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Care settings
How CMS programs treat this code. These are CMS claim edits and list entries, not coverage or eligibility rules.
Hospice: not accepted as primary
Not accepted as the principal diagnosis on a hospice claim (bill types 081x and 082x). The Integrated OCE returns an edit for this code.
Reason: Manifestation code. Report the underlying condition first (see the Code first note).
Hospital CC
Counts as a complication or comorbidity (CC) when reported as a secondary diagnosis on an inpatient claim. It does not count when the principal diagnosis is one of the 25 codes in its exclusion list. Some MS-DRGs also ignore a CC or MCC that defines the DRG.
Source: CMS MS-DRG Definitions Manual v44, effective October 1, 2026, Appendix CAlphabetic Index terms
Terms the official Alphabetic Index lists for this code. 6 entries
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), amyloidosis
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), endocrine disease NEC
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), gout
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), hyperthyroidism
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), hyperthyroidism, with thyroid storm
- Neuropathy, neuropathic, peripheral (nerve), autonomic, in (due to), metabolic disease NEC