E83.82
Disorders of pyrophosphate metabolism
E83.82 is a non-billable ICD-10-CM code header for disorders of pyrophosphate metabolism. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are E83.820 Generalized arterial calcification of infancy with unspecified genetic causality, E83.821 ENPP1 deficiency causing generalized arterial calcification of infancy, E83.822 ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2, E83.823 ABCC6 deficiency causing generalized arterial calcification of infancy and 2 more. Its coding notes include 9 Excludes1 entries and 1 Excludes2 entry.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- dietary mineral deficiency (E58-E61)
- parathyroid disorders (E20-E21)
- vitamin D deficiency (E55.-)
Also from chapter/block level (6 notes)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Notes
Also from chapter/block level (1 note)
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
More specific codes under E83.82 6
- E83.820Generalized arterial calcification of infancy with unspecified genetic causalityBillable
- E83.821ENPP1 deficiency causing generalized arterial calcification of infancyBillable
- E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2Billable
- E83.823ABCC6 deficiency causing generalized arterial calcification of infancyBillable
- E83.824ABCC6 deficiency causing pseudoxanthoma elasticumBillable
- E83.825CD73 deficiency causing arterial calcificationBillable