H49.81
Kearns-Sayre syndrome
H49.81 is a non-billable ICD-10-CM code header for kearns-Sayre syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are H49.811 Kearns-Sayre syndrome, right eye; H49.812 Kearns-Sayre syndrome, left eye; H49.813 Kearns-Sayre syndrome, bilateral and H49.819 Kearns-Sayre syndrome, unspecified eye. Its coding notes include a Code also instruction and 15 Excludes2 entries.
Code also
Two codes may be needed to describe the condition. This note gives no sequencing order.
- , if applicable, other manifestations, such as:
- heart block (I45.9)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (12 notes)
- nystagmus and other irregular eye movements (H55)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Inclusion terms
Conditions classified to this code.
- Progressive external ophthalmoplegia with pigmentary retinopathy
Notes
Also from chapter/block level (1 note)
- Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 3 entries