H49.4
Progressive external ophthalmoplegia
H49.4 is a non-billable ICD-10-CM code header for progressive external ophthalmoplegia. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are H49.40 Progressive external ophthalmoplegia, unspecified eye; H49.41 Progressive external ophthalmoplegia, right eye; H49.42 Progressive external ophthalmoplegia, left eye and H49.43 Progressive external ophthalmoplegia, bilateral. Its coding notes include 1 Excludes1 entry and 15 Excludes2 entries.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
- Kearns-Sayre syndrome (H49.81-)
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (12 notes)
- nystagmus and other irregular eye movements (H55)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Notes
Also from chapter/block level (1 note)
- Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 2 entries