Q99.81
Usher syndrome
Q99.81 is a non-billable ICD-10-CM code header for usher syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q99.811 Usher syndrome, type 1; Q99.812 Usher syndrome, type 2; Q99.813 Usher syndrome, type 3; Q99.818 Other Usher syndrome and 1 more. Its coding notes include a Use additional code instruction and 2 Excludes2 entries.
Guidelines tip
From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.
Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.
Use additional code
Add the listed code as a secondary code, if known.
- code to identify any auditory and visual manifestations
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Also from chapter/block level (2 notes)
- mitochondrial metabolic disorders (E88.4-)
- inborn errors of metabolism (E70-E88)
Notes
Also from chapter/block level (1 note)
- Codes from this chapter are not for use on maternal records