Q42

Congenital absence, atresia and stenosis of large intestine

FY2027Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders/Q38–Q45 Other congenital malformations of the digestive system

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

Q42 is a non-billable ICD-10-CM code category for congenital absence, atresia and stenosis of large intestine. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are Q42.0 Congenital absence, atresia and stenosis of rectum with fistula; Q42.1 Congenital absence, atresia and stenosis of rectum without fistula; Q42.2 Congenital absence, atresia and stenosis of anus with fistula; Q42.3 Congenital absence, atresia and stenosis of anus without fistula and 2 more. Its coding notes include 1 Excludes2 entry.

Guidelines tip

From the FY2027 Official Guidelines. ICD10Ref adds no rules of its own.

Chapter 17 codes can be used for life. Manifestations that are an inherent part of a specifically coded anomaly are not coded separately. A corrected malformation is reported with a personal history code.

Guidelines I.C.17Congenital malformations and genetic disordersRead the official text

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • inborn errors of metabolism (E70-E88)

Includes

Further defines or gives examples of the content of the category.

This code
  • congenital obstruction, occlusion and stricture of large intestine

Notes

Also from chapter/block level (1 note)
Inherited from Chapter 17 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
  • Codes from this chapter are not for use on maternal records

More specific codes under Q42 6