M04
Autoinflammatory syndromes
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
M04 is a non-billable ICD-10-CM code category for autoinflammatory syndromes. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are M04.1 Periodic fever syndromes, M04.2 Cryopyrin-associated periodic syndromes, M04.3 VEXAS syndrome, M04.8 Other autoinflammatory syndromes and 1 more. Its coding notes include 11 Excludes2 entries.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
This code
- Crohn's disease (K50.-)
Also from chapter/block level (10 notes)
Inherited from Chapter 13 Diseases of the musculoskeletal system and connective tissue
- arthropathic psoriasis (L40.5-)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- compartment syndrome (traumatic) (T79.A-)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Notes
Also from chapter/block level (1 note)
Inherited from Chapter 13 Diseases of the musculoskeletal system and connective tissue
- Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition