G71.03

Limb girdle muscular dystrophies

FY2027Chapter 6: Diseases of the nervous system/G70–G73 Diseases of myoneural junction and muscle

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

G71.03 is a non-billable ICD-10-CM code header for limb girdle muscular dystrophies. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are G71.031 Autosomal dominant limb girdle muscular dystrophy, G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction, G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction, G71.034 Limb girdle muscular dystrophy due to sarcoglycan dysfunction and 4 more. Its coding notes include 11 Excludes2 entries.

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from G71 Primary disorders of muscles
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
Also from chapter/block level (8 notes)
Inherited from Chapter 6 Diseases of the nervous system
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

More specific codes under G71.03 8