G40.83
Dravet syndrome
Non-billable headerNot valid on its own. Use one of the more specific codes under it.
G40.83 is a non-billable ICD-10-CM code header for dravet syndrome. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are G40.833 Dravet syndrome, intractable, with status epilepticus and G40.834 Dravet syndrome, intractable, without status epilepticus. Its coding notes include 5 Excludes1 entries and 12 Excludes2 entries.
Excludes1
Not coded here. The listed conditions generally should not be reported together.
Excludes2
Not included here. Both codes may be reported if the patient has both conditions.
Inherited from G40 Epilepsy and recurrent seizures
Also from chapter/block level (8 notes)
Inherited from Chapter 6 Diseases of the nervous system
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Inclusion terms
Conditions classified to this code.
This code
- Polymorphic epilepsy in infancy (PMEI)
- Severe myoclonic epilepsy in infancy (SMEI)
Notes
Inherited from G40 Epilepsy and recurrent seizures
- the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Alphabetic Index terms
Terms the official Alphabetic Index lists for this code. 4 entries
- Epilepsy, epileptic, epilepsia (attack) (cerebral) (convulsion) (fit) (seizure), myoclonus, myoclonic, severe, in infancy (SMEI)
- Epilepsy, epileptic, epilepsia (attack) (cerebral) (convulsion) (fit) (seizure), polymorphic, in infancy (PMEI)
- PMEI (polymorphic epilepsy in infancy)
- SMEI (severe myoclonic epilepsy in infancy)