C7A.0

Malignant carcinoid tumors

FY2027Chapter 2: Neoplasms/C7A Malignant neuroendocrine tumors

Non-billable headerNot valid on its own. Use one of the more specific codes under it.

C7A.0 is a non-billable ICD-10-CM code header for malignant carcinoid tumors. Report a more specific code from it instead. It is part of the FY2027 code set, effective October 1, 2026. The more specific codes under it are C7A.00 Malignant carcinoid tumor of unspecified site; C7A.01 Malignant carcinoid tumors of the small intestine; C7A.02 Malignant carcinoid tumors of the appendix, large intestine, and rectum and C7A.09 Malignant carcinoid tumors of other sites. Its coding notes include a Use additional code instruction, a Code also instruction and 2 Excludes2 entries.

Use additional code

Add the listed code as a secondary code, if known.

Inherited from C7A Malignant neuroendocrine tumors
  • code to identify any associated endocrine syndrome, such as:

Code also

Two codes may be needed to describe the condition. This note gives no sequencing order.

Inherited from C7A Malignant neuroendocrine tumors
  • any associated multiple endocrine neoplasia [MEN] syndromes (E31.2-)

Excludes2

Not included here. Both codes may be reported if the patient has both conditions.

Inherited from C7A Malignant neuroendocrine tumors
  • malignant pancreatic islet cell tumors (C25.4)
  • Merkel cell carcinoma (C4A.-)

Notes

Also from chapter/block level (8 notes)
Inherited from Chapter 2 Neoplasms
  • Functional activity
  • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Morphology [Histology]
  • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Primary malignant neoplasms overlapping site boundaries
  • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Malignant neoplasm of ectopic tissue
  • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

More specific codes under C7A.0 4